Neurosurgical Diseases and Disorders (M-Z) / Spinal Cord Lipomas & Lipomyelomeningoceles
Spinal
cord lipomas and lipomyelomeningoceles are both associated with abnormal fat
accumulation in and around the spinal cord.
Lipomas
- General Information
- A spinal cord lipoma is fat within the normally positioned spinal cord
without any skin or bony abnormalities.
- Most commonly these rare lesions are located within the thoracic spinal
cord.
- They may be symptomatic and appear most often in
adults.
- Symptoms
- Spinal cord compression can cause numbness and
tingling, weakness, difficulty with urinating or bowel movements,
incontinence, and stiffness of the extremities.
- Treatment
- A laminectomy is performed to gain access to the spinal cord. The goal
of surgery is to reduce the size of the lipoma, not total removal of the
fat. No other treatment method is recommended.
Lipomyelomeningocele
- General Information
- This is a lesion present at birth that is associated with spina bifida
(congenital failure of the spinal bones to close).
- The condition is associated with abnormal fat accumulation that starts
below the skin and extends through the bony opening to the spinal cord.
- These lesions become evident within the first few
months to years of life and affect females more than males in a 1.5 to 1
ratio.
- Symptoms
- More than 90 percent of patients will have an obvious soft tissue
swelling over the spine in the lower back. These lesions are covered by skin
and are not painful.
- Patients may lose neurological function within the first few weeks after
birth but more typically function deteriorates over a period of months to
years.
- Neurological symptoms usually include weakness, and bladder and bowel
incontinence. The weakness may be symmetrical or asymmetrical and may result
in atrophy of the lower extremities.
- In older adolescents and adults, pain may be the
driving force to bring the patient to a doctor. The pain may radiate and be
difficult to describe. Back mobility may be limited.
- Diagnosis
- MRI has become the imaging procedure of choice for lipomyelomeningoceles
and spinal cord lipomas. These scans give extraordinary anatomical details
that help the surgeon plan the operative procedure.
- Plain x-rays show spina bifida in most cases.
- Treatment
- The goals of surgery are to release the attachment of the fat
(tethering) to the spinal cord and reduce the bulk of the fatty tumor.
- Simple cosmetic treatment does not prevent
neurologic difficulties and may make later, more complete treatment
difficult.
- Surgical treatment is recommended when the patient
reaches age 2 months or at the time of diagnosis if symptoms occur at a
later age.
- Outcome
- With surgery, 19 percent of patients will improve, 75 percent will be
unchanged, and 6 percent will worsen.
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